Shafritz A B, Kaplan F S
Department of Orthopaedic Surgery, University of Pennsylvania School of Medicine, Philadelphia 19104, USA.
Clin Orthop Relat Res. 1998 Jan(346):46-52.
Fibrodysplasia ossificans progressiva, myositis ossificans traumatica, and osteogenic sarcoma are representative genetic, traumatic, and neoplastic disorders of osteogenesis, respectively. However, the pathology, pathophysiology, and natural history of the disorders differ substantially. Gene expression related to bone induction was studied in these disorders. Primary cell lines established from lesional tissues derived from each of these disorders expressed different patterns of protooncogenes, bone morphogenetic protein genes, and bone phenotype specific genes. The osteogenic sarcoma cell line expressed the entire repertoire bone morphogenetic proteins 1 to 7, c-fos and c-jun messenger ribonucleic acids. Myositis ossificans traumatica cells expressed phenotype markers similar to those of the osteogenic sarcoma cells, and expressed bone morphogenetic proteins 1, 4, and 6 and c-fos messenger ribonucleic acids, but not c-jun messenger ribonucleic acid. Fibrodysplasia ossificans progressiva early lesional cells demonstrated specific over-expression of bone morphogenetic protein 4 messenger ribonucleic acid. Differential expression of genes related to osteogenesis have important implications for understanding the earliest molecular events in normal and dysregulated osteogenesis in humans.
进行性骨化性纤维发育不良、创伤性骨化性肌炎和成骨肉瘤分别是成骨的典型遗传性、创伤性和肿瘤性疾病。然而,这些疾病的病理学、病理生理学和自然病史有很大差异。对这些疾病中与骨诱导相关的基因表达进行了研究。从这些疾病各自的病变组织建立的原代细胞系表达了不同模式的原癌基因、骨形态发生蛋白基因和骨表型特异性基因。成骨肉瘤细胞系表达了骨形态发生蛋白1至7、c-fos和c-jun信使核糖核酸的全部组合。创伤性骨化性肌炎细胞表达与成骨肉瘤细胞相似的表型标志物,并表达骨形态发生蛋白1、4和6以及c-fos信使核糖核酸,但不表达c-jun信使核糖核酸。进行性骨化性纤维发育不良早期病变细胞显示骨形态发生蛋白4信使核糖核酸的特异性过表达。与成骨相关基因的差异表达对于理解人类正常和成骨失调中最早的分子事件具有重要意义。