Kanemoto Y, Ochiai C, Yoshimoto Y, Nagai M
Department of Neurosurgery, Dokkyo University School of Medicine, Tochigi, Japan.
Surg Neurol. 1998 May;49(5):534-7. doi: 10.1016/s0090-3019(97)00284-x.
There have been no detailed descriptions of the clinical symptoms of a primarily extracranial jugular foramen neurinoma (JFN), because this type of tumor is extremely rare.
Although the 51-year-old woman presented with only mild complaints of dysphagia and hoarseness, neurologic examination revealed marked left hemiatrophy of the tongue. Although magnetic resonance imaging suggested a JFN, the patient's mild symptoms and normal jugular foramen were potentially misleading in the diagnosis of this patient. Surgical exploration demonstrated that the tumor originated from the extracranial portion of the 10th cranial nerve, extending into the jugular foramen. Subtotal resection ameliorated the 12th cranial nerve palsy.
The authors present a case of a primarily extracranial JFN manifesting as a 12th nerve palsy. The clinical symptoms and signs produced by a tumor in this extremely rare location are discussed.
原发性颅外颈静脉孔神经鞘瘤（JFN）的临床症状尚无详细描述，因为这类肿瘤极为罕见。
尽管这位51岁女性仅表现出轻度吞咽困难和声音嘶哑，但神经系统检查发现其舌左侧明显萎缩。虽然磁共振成像提示为颈静脉孔神经鞘瘤，但患者的轻微症状和正常的颈静脉孔在该患者的诊断中可能产生误导。手术探查显示肿瘤起源于第10颅神经的颅外部分，延伸至颈静脉孔。次全切除改善了第12颅神经麻痹。
作者报告了一例以第12神经麻痹为表现的原发性颅外颈静脉孔神经鞘瘤病例。讨论了这种极为罕见部位的肿瘤所产生的临床症状和体征。
