The neurocutaneous syndromes are a diverse group of diseases characterized by widespread abnormalities in structures of ectodermal origin, including the skin, eye, and central and peripheral nervous systems. These syndromes are particularly interesting to the clinician because they often present with cutaneous signs at birth or very early in life. These skin markers may be clues to widespread abnormality that may later develop in the nervous system and other areas of the body, making early diagnosis from careful assessment of cutaneous signs a particularly challenging task. Six of the most common of these syndromes are reviewed.
神经皮肤综合征是一组多样的疾病,其特征是外胚层起源的结构广泛异常,包括皮肤、眼睛以及中枢和周围神经系统。这些综合征对临床医生来说特别有趣,因为它们常常在出生时或生命早期就出现皮肤体征。这些皮肤标记可能是广泛异常的线索,这些异常可能随后在神经系统和身体其他部位发展,使得通过仔细评估皮肤体征进行早期诊断成为一项特别具有挑战性的任务。本文综述了其中六种最常见的综合征。