Scommegna S, Mastrangelo S, Lazzareschi I, Ruggiero A
Divisione di Oncologia Pediatrica, Università Cattolica del Sacro Cuore di Roma.
Pediatr Med Chir. 1997 Nov-Dec;19(6):473-5.
Rhabdoid tumor of the kidney (RTK) is a quite rare malignant neoplasm of early childhood. It has a very unfavourable prognosis, since it tends to give early metastases and shows a poor response to chemotherapy regimens. We report a case of an infant with RTK, who had a rapidly progressive course. Based upon our case and the review of the literature, we would like to stress the importance of a differential diagnosis with another kidney cancer, namely Wilms tumor, which is more frequent and has by far a better prognosis.
肾横纹肌样瘤(RTK)是一种儿童早期极为罕见的恶性肿瘤。其预后非常差,因为它易于早期转移,并且对化疗方案反应不佳。我们报告一例患有肾横纹肌样瘤的婴儿病例,该病例病情进展迅速。基于我们的病例以及文献回顾,我们想强调与另一种肾癌(即威尔姆斯瘤)进行鉴别诊断的重要性,威尔姆斯瘤更为常见,且预后要远好得多。