Pereira I A, Pereira R M, Borba E F, Gonçalves C R, Yoshinari N Y, Cossermelli W
Disciplina de Reumatologia do Hospital das Clínicas, Faculdade de Medicina, Universidade de São Paulo.
Rev Assoc Med Bras (1992). 1997 Oct-Dec;43(4):311-3. doi: 10.1590/s0104-42301997000400006.
Hypocomplementaemic urticarial vasculitis syndrome is a leukocytoclastic vasculitis characterized by urticarial lesions, associated with fever, arthralgias, arthritis and abdominal pain. Other systemic manifestations include glomerulonephritis, uveitis, episcleritis, chronic obstructive pulmonary disease and neurological abnormalities. Some case associated with systemic lupus erythematosus have been described and SLE diagnosis was made by previous or concomitant diagnostic criteria before onset of urticarial vasculitis. Urticarial vasculitis prior to SLE diagnosis is rare. The development of anti-Ro/SS-A antibody for the diagnosis of SLE is emphasized. The authors alert to the importance of periodically searching for this marker in patients with urticarial vasculitis.
低补体血症性荨麻疹性血管炎综合征是一种白细胞破碎性血管炎,其特征为荨麻疹样皮损,伴有发热、关节痛、关节炎和腹痛。其他全身表现包括肾小球肾炎、葡萄膜炎、巩膜炎、慢性阻塞性肺疾病和神经异常。已描述了一些与系统性红斑狼疮相关的病例,且在荨麻疹性血管炎发作前根据既往或同时存在的诊断标准作出了系统性红斑狼疮的诊断。在系统性红斑狼疮诊断之前出现荨麻疹性血管炎的情况罕见。强调了抗Ro/SS - A抗体用于系统性红斑狼疮诊断的作用。作者提醒在荨麻疹性血管炎患者中定期寻找该标志物的重要性。