Turra S, Santini S, Cagnoni G, Jacopetti T
Institute of Clinical Orthopaedics, University of Padova and the General Hospital of Padova, Italy.
J Pediatr Orthop. 1998 May-Jun;18(3):337-45.
We report our experience in seven patients with congenital gigantism of the foot with the following diagnoses: neurofibromatosis (two), fibrolipomatosis (two), Proteus syndrome (two), and idiopathic localized gigantism (one). Our purpose is to introduce a new classification of foot gigantism, based on the concept of "neuroinduction." In our experience, intraoperative examination and subsequent histologic examination show consistently pathologic findings in the plantar nerve and its terminal branches in the foot affected by gigantism. Limited surgical treatment was used in five patients. To prevent forefoot enlargement and recurrence of deformity, we suggest complete ray resection. We evaluated our results using radiographs, functional status, and cosmetic considerations.
我们报告了7例足部先天性巨大症患者的治疗经验,其诊断如下:神经纤维瘤病(2例)、纤维脂肪瘤病(2例)、普洛提斯综合征(2例)和特发性局限性巨大症(1例)。我们的目的是基于“神经诱导”概念引入一种新的足部巨大症分类方法。根据我们的经验,术中检查及随后的组织学检查显示,在受巨大症影响的足部,足底神经及其终末分支始终存在病理改变。5例患者采用了有限的手术治疗。为防止前足增大和畸形复发,我们建议行完整的射线切除。我们通过X线片、功能状态和美观因素来评估治疗结果。