Karol L A, Haideri N F, Halliday S E, Smitherman T B, Johnston C E
Texas Scottish Rite Hospital for Children, Dallas 75219, USA.
J Pediatr Orthop. 1998 May-Jun;18(3):381-6.
Twelve patients with healed congenital pseudarthrosis of the tibia underwent gait analysis and muscle strength testing to determine the functional result of treatment. Six children younger than 4 years of age presented with pseudarthroses (early onset), and six children first fractured at older than 4 years of age (delayed onset). Four children with amputations as final treatment for congenital pseudarthrosis were studied for comparison. The early-onset group had undergone an average of 4.2 surgeries and all required transankle fixation. The delayed-onset group had undergone an average of 1.5 surgeries, with one child requiring fixation across the ankle. Lack of ankle push-off and foot drop occurred in the early-onset group. Terminal stance phase ankle power generation was greatly diminished in the early-onset group. Total mechanical work performed by the affected limb, when compared to the uninvolved contralateral limb, was symmetric in delayed-onset patients and reduced by 68% in early-onset patients and by 85% in amputees. Gastrocsoleus strength was reduced by 40%. Gait and muscle strength of patients with "healed" congenital pseudarthrosis of the tibia are markedly disturbed. Early onset of disease, early surgery, and transankle fixation lead to an inefficient gait comparable to that of amputees.
12例胫骨先天性假关节已愈合的患者接受了步态分析和肌肉力量测试,以确定治疗的功能结果。6名4岁以下儿童患有假关节(早发型),6名儿童在4岁以上首次骨折(迟发型)。研究了4例接受截肢作为先天性假关节最终治疗的儿童以作比较。早发型组平均接受了4.2次手术,且均需要经踝关节固定。迟发型组平均接受了1.5次手术,其中1名儿童需要跨踝关节固定。早发型组出现踝关节蹬离缺失和足下垂。早发型组终末站立期踝关节产生的力量大幅减弱。与未受累的对侧肢体相比,迟发型患者患侧肢体完成的总机械功对称,早发型患者患侧肢体总机械功减少68%,截肢患者减少85%。腓肠肌力量降低了40%。胫骨“愈合”的先天性假关节患者的步态和肌肉力量明显受到干扰。疾病早发、早期手术和经踝关节固定导致步态效率低下,与截肢患者相当。