Truhlar S, Roth A
University of Kansas School of Medicine-Kansas City, USA.
Kans Med. 1998;98(3):18-9.
A case of diffuse pulmonary ossification in association with congenital protein C deficiency is presented. We propose that multiple pulmonary thrombi secondary to a long-term hypercoagulable state produced pulmonary ischemia that predisposed to intralveolar ossification.
本文报告一例与先天性蛋白C缺乏相关的弥漫性肺骨化病例。我们认为,长期高凝状态继发的多发性肺血栓形成导致了肺缺血,进而易引发肺泡内骨化。