Tinschert S, Braun H S
Institute of Medical Genetics, School of Medicine (Charité), Humboldt University, Berlin, Germany.
Am J Med Genet. 1998 May 18;77(3):175-81. doi: 10.1002/(sici)1096-8628(19980518)77:3<175::aid-ajmg1>3.0.co;2-p.
Craniometaphyseal dysplasia (CMD) was found in 6 generations of a large German kindred; 24 affected individuals were identified. The clinical diagnosis was confirmed by further examinations in 15 individuals, including 2 exhumed skeletons. Five deceased individuals were considered to be undoubtedly affected by reviewing photographs, and 4 must have had CMD from genealogical considerations. Pedigree analysis was performed over 8 generations back to persons born at the beginning of the 18th century in a central area of Germany. The trait could be traced back to a common male ancestor, born in 1790. Molecular genetic investigations on 3 generations of this kindred are in progress. In the present study we describe the clinical characteristics of the family.