Horowitz S, Thomas C, Gruener G, Nand S, Shea J F
Department of Radiology, Loyola University Medical Center, Maywood, Ill 60153, USA.
AJNR Am J Neuroradiol. 1998 May;19(5):900-2.
We report an unusual cause of leptomeningeal MR enhancement, amyloid, along the surfaces of the spinal cord and brain stem and in the spinal subarachnoid space, with sacral intradural and epidural deposition. Type I familial amyloid polyneuropathy may cause amyloid deposition along the leptomeninges of the spinal cord and brain in addition to the visceral organs and the peripheral somatic and autonomic nerves.
我们报告了一种软脑膜磁共振成像强化的罕见病因——淀粉样蛋白，其沉积于脊髓和脑干表面、脊髓蛛网膜下腔，以及骶部硬脊膜内和硬脊膜外。I型家族性淀粉样多神经病除了可导致内脏器官、外周躯体神经和自主神经出现淀粉样蛋白沉积外，还可引起脊髓和脑软脑膜的淀粉样蛋白沉积。
