• 文献检索
  • 文档翻译
  • 深度研究
  • 学术资讯
  • Suppr Zotero 插件Zotero 插件
  • 邀请有礼
  • 套餐&价格
  • 历史记录
应用&插件
Suppr Zotero 插件Zotero 插件浏览器插件Mac 客户端Windows 客户端微信小程序
定价
高级版会员购买积分包购买API积分包
服务
文献检索文档翻译深度研究API 文档MCP 服务
关于我们
关于 Suppr公司介绍联系我们用户协议隐私条款
关注我们

Suppr 超能文献

核心技术专利：CN118964589B侵权必究
粤ICP备2023148730 号-1Suppr @ 2026

文献检索

告别复杂PubMed语法，用中文像聊天一样搜索，搜遍4000万医学文献。AI智能推荐，让科研检索更轻松。

立即免费搜索

文件翻译

保留排版，准确专业，支持PDF/Word/PPT等文件格式，支持 12+语言互译。

免费翻译文档

深度研究

AI帮你快速写综述，25分钟生成高质量综述，智能提取关键信息，辅助科研写作。

立即免费体验

The hyper-IgM (HIM) syndrome.

作者信息

Ramesh N, Seki M, Notarangelo L D, Geha R S

机构信息

Division of Immunology, Children's Hospital, Harvard Medical School, Boston, MA 02115-5747, USA.

出版信息

Springer Semin Immunopathol. 1998;19(4):383-99. doi: 10.1007/BF00792598.

DOI:10.1007/BF00792598
PMID:9618764
Abstract
摘要

相似文献

1
The hyper-IgM (HIM) syndrome.高IgM综合征
Springer Semin Immunopathol. 1998;19(4):383-99. doi: 10.1007/BF00792598.
2
Localization of the genetic defect in X-linked immunoglobulin deficiency with normal or elevated IgM (HIGMX-1) to the CD40 ligand gene.X连锁免疫球蛋白缺陷伴IgM正常或升高（HIGMX-1）的基因缺陷定位于CD40配体基因。
Trans Assoc Am Physicians. 1993;106:91-5.
3
IgM-restricted production of immunoglobulin by lymphoid cell lines from patients with immunodeficiency with hyper IgM (dysgammaglobulinemia).来自高IgM免疫缺陷（异常丙种球蛋白血症）患者的淋巴细胞系对免疫球蛋白的IgM限制性产生。
Clin Immunol Immunopathol. 1981 Apr;19(1):91-7. doi: 10.1016/0090-1229(81)90050-7.
4
[Lymphocyte study in the selective deficit of IgA].
Recenti Prog Med. 1984 Dec;75(12):1061-75.
5
Hyper IgM syndrome associated with defective CD40-mediated B cell activation.与CD40介导的B细胞活化缺陷相关的高IgM综合征。
J Clin Invest. 1994 Oct;94(4):1404-9. doi: 10.1172/JCI117476.
6
[Hypogammaglobulinemia G and A with hypergammaglobulinemia M. Apropos of 12 cases].低丙种球蛋白血症G和A伴高丙种球蛋白血症M。附12例报告
Arch Fr Pediatr. 1990 May;47(5):345-9.
7
Hyper IgM immunodeficiency. A primary dysfunction of B lymphocyte isotype switching.高IgM免疫缺陷。B淋巴细胞同种型转换的原发性功能障碍。
J Clin Invest. 1983 Nov;72(5):1650-7. doi: 10.1172/JCI111124.
8
Differential requirements for expression of CD80/86 and CD40 on B cells for T-dependent antibody responses in vivo.体内T细胞依赖性抗体应答中B细胞上CD80/86和CD40表达的差异需求。
J Immunol. 2003 Jan 15;170(2):781-7. doi: 10.4049/jimmunol.170.2.781.
9
[Primary deficiencies in antibody synthesis. II. Dysgammaglobulinemias].
Bol Med Hosp Infant Mex. 1983 May;40(5):223-42.
10
Evidence for a defect in "switch" T cells in patients with immunodeficiency and hyperimmunoglobulinemia M.免疫缺陷和高免疫球蛋白M血症患者中“转换”T细胞存在缺陷的证据。
N Engl J Med. 1986 Feb 13;314(7):409-13. doi: 10.1056/NEJM198602133140703.

引用本文的文献

1
Novel Functions of Integrins as Receptors of CD154: Their Role in Inflammation and Apoptosis.整合素作为 CD154 受体的新功能：在炎症和细胞凋亡中的作用。
Cells. 2022 May 25;11(11):1747. doi: 10.3390/cells11111747.
2
Recurrent Gallbladder Hydrops and Sclerosing Cholangitis in 11-Year-Old Male with Hyper IgM Syndrome.患有高IgM综合征的11岁男性复发性胆囊积水和硬化性胆管炎
Iran J Pediatr. 2013 Dec;23(6):705-6.
3
Platelet-associated CD40/CD154 mediates remote tissue damage after mesenteric ischemia/reperfusion injury.血小板相关 CD40/CD154 介导肠缺血/再灌注损伤后的远处组织损伤。

本文引用的文献

1
Classification of mutations in the human CD40 ligand, gp39, that are associated with X-linked hyper IgM syndrome.与X连锁高IgM综合征相关的人类CD40配体gp39突变的分类。
Protein Sci. 1996 Mar;5(3):531-4. doi: 10.1002/pro.5560050316.
2
PNEUMOCYSTIS CARINII PNEUMONIA AND CONGENITAL HYPOGAMMAGLOBULINAEMIA.卡氏肺孢子虫肺炎与先天性低丙种球蛋白血症
Arch Dis Child. 1964 Feb;39(203):18-25. doi: 10.1136/adc.39.203.18.
3
Antibody deficiency syndrome associated with beta-2 macroglobulinemia.与β-2微球蛋白血症相关的抗体缺陷综合征。
PLoS One. 2012;7(2):e32260. doi: 10.1371/journal.pone.0032260. Epub 2012 Feb 27.
4
Gastrointestinal Manifestations of Non-AIDS Immunodeficiency.非艾滋病免疫缺陷的胃肠道表现
Curr Treat Options Gastroenterol. 2002 Feb;5(1):17-25. doi: 10.1007/s11938-002-0003-4.
5
X-linked hyper IgM syndrome.X连锁高IgM综合征
Clin Rev Allergy Immunol. 2000 Oct;19(2):205-15. doi: 10.1385/CRIAI:19:2:205.
6
Induction of functional CD154 (CD40 ligand) in neonatal T cells by cAMP-elevating agents.通过提高环磷酸腺苷（cAMP）的试剂诱导新生儿T细胞中功能性CD154（CD40配体）的产生。
Immunology. 2000 Aug;100(4):432-40. doi: 10.1046/j.1365-2567.2000.00051.x.
J Pediatr. 1962 Dec;61:831-42. doi: 10.1016/s0022-3476(62)80193-0.
4
Recurrent bacterial infections and dysgamma-globulinemia: deficiency of 7S gamma-globulins in the presence of elevated 19S gamma-globulins. Report of two cases.复发性细菌感染与γ-球蛋白异常血症：19Sγ-球蛋白升高时7Sγ-球蛋白缺乏。两例报告。
Pediatrics. 1961 Aug;28:182-95.
5
Clinical spectrum of X-linked hyper-IgM syndrome.X连锁高IgM综合征的临床谱
J Pediatr. 1997 Jul;131(1 Pt 1):47-54. doi: 10.1016/s0022-3476(97)70123-9.
6
Suppression of murine thyroiditis via blockade of the CD40-CD40L interaction.通过阻断CD40-CD40L相互作用抑制小鼠甲状腺炎
Immunology. 1997 Mar;90(3):421-6. doi: 10.1111/j.1365-2567.1997.00421.x.
7
Jak3 is associated with CD40 and is critical for CD40 induction of gene expression in B cells.Jak3与CD40相关联，并且对于B细胞中CD40诱导基因表达至关重要。
Immunity. 1997 Apr;6(4):379-87. doi: 10.1016/s1074-7613(00)80281-2.
8
Functional CD40 ligand is expressed on human vascular endothelial cells, smooth muscle cells, and macrophages: implications for CD40-CD40 ligand signaling in atherosclerosis.功能性CD40配体在人血管内皮细胞、平滑肌细胞和巨噬细胞上表达：对动脉粥样硬化中CD40-CD40配体信号传导的影响。
Proc Natl Acad Sci U S A. 1997 Mar 4;94(5):1931-6. doi: 10.1073/pnas.94.5.1931.
9
The CD40 ligand. At the center of the immune universe?CD40配体。处于免疫世界的中心？
Immunol Res. 1997 Feb;16(1):59-70. doi: 10.1007/BF02786323.
10
The role of CD40 ligand in costimulation and T-cell activation.CD40配体在共刺激和T细胞活化中的作用。
Immunol Rev. 1996 Oct;153:85-106. doi: 10.1111/j.1600-065x.1996.tb00921.x.