Haidú J, Marton G T, Papp C, Szabó I, Cesko I, Papp Z
I. sz. Szülészeti és Nögyógyászati Klinika, Semmelweis Orvostudományi Egyetem, Budapest.
Orv Hetil. 1998 May 17;139(20):1219-22.
Tricuspid atresia is the third most common cyanotic cardiac malformation, seen in 1 per cent of children with congenital heart disease. It occurs in 4-5 per cent of congenital heart defects diagnosed prenatally, this difference is a consequence of a high percentage of intrauterine death these severely ill fetuses. Initial surgical treatment is palliation, usually with aortopulmonary shunt. Definitive treatment is the Fontan operation, when the systemic venous return is connected directly to the pulmonary tree. Five-year survival for liveborn patients is 50, but for prenatally diagnosed fetuses only 20%. In Hungary there is only a few survivor. Authors have diagnosed 20 tricuspid atresias during a five-year period by fetal echocardiography. In two cases the postnatal findings were: normal tricuspid valves, univentricular atrio-ventricular connection and stenosis of the pulmonary artery, in one case dysplastic tricuspid valves, hypoplastic right ventricle and stenosis of the pulmonary artery. Authors summarise their experiences with prenatal echocardiography of tricuspid atresia and describe characteristic signs could be found by routine ultrasound screening of this severe cardiac malformation.
三尖瓣闭锁是第三常见的青紫型心脏畸形，在先天性心脏病患儿中占1%。它在产前诊断的先天性心脏缺陷中占4 - 5%，这种差异是由于这些重症胎儿的宫内死亡率较高。初始手术治疗是姑息治疗，通常采用体肺分流术。确定性治疗是Fontan手术，即将体循环静脉回流直接连接到肺循环。活产患者的五年生存率为50%，但产前诊断的胎儿仅为20%。在匈牙利，幸存者寥寥无几。作者在五年期间通过胎儿超声心动图诊断出20例三尖瓣闭锁。两例产后发现为：三尖瓣正常，房室单心室连接和肺动脉狭窄；一例为发育异常的三尖瓣、右心室发育不良和肺动脉狭窄。作者总结了他们在三尖瓣闭锁产前超声心动图方面的经验，并描述了通过常规超声筛查这种严重心脏畸形时可发现的特征性征象。
