Esaki M, Kagawa K, Noda T, Nishigaki K, Gotoh K, Fujiwara H, Nitta T, Kumada Y, Murakawa S, Hirose H, Mochida Y, Kimura K, Maehara T, Hara M
Second Department of Internal Medicine, Gifu University School of Medicine.
Intern Med. 1998 Apr;37(4):370-5. doi: 10.2169/internalmedicine.37.370.
Leiomyosarcomas are extremely rare primary cardiac tumors. We report a rapidly growing primary leiomyosarcoma of the right ventricle, which obstructed the right ventricular outflow tract within one month after symptom onset in a 68-year-old man. Two-dimensional echocardiography was useful in diagnosing the extent and progression of the tumor. The tumor was surgically resected on an emergency basis, and the right ventricle and pulmonary artery were successfully reconstructed. Recurrence of the tumor on the right ventricle was observed, and the patient was overcome by sudden dyspnea and died three months after surgery.
平滑肌肉瘤是极其罕见的原发性心脏肿瘤。我们报告一例右心室原发性平滑肌肉瘤迅速生长的病例,该肿瘤在一名68岁男性出现症状后1个月内阻塞了右心室流出道。二维超声心动图有助于诊断肿瘤的范围和进展情况。该肿瘤在紧急情况下接受了手术切除,右心室和肺动脉成功重建。观察到肿瘤在右心室复发,患者术后3个月因突发呼吸困难而死亡。