Lemes V, Murphy A M, Osterman F A, Laschinger J C, Kan J S
Department of Pediatrics, Division of Pediatric Cardiology, The Johns Hopkins Hospital, 600 North Wolfe Street, Brady 5, Baltimore, MD 21287, USA.
Pediatr Cardiol. 1998 Jul-Aug;19(4):355-7. doi: 10.1007/s002469900322.
We describe a patient with protein-losing enteropathy who presented 6 months after undergoing a modified Fontan operation. After failing to respond to medical therapy, the Fontan tunnel was fenestrated by catheter intervention with immediate improvement and resolution of hypoproteinemia and enteric protein loss.
我们描述了一名患有蛋白丢失性肠病的患者,该患者在接受改良Fontan手术后6个月出现症状。在药物治疗无效后,通过导管介入对Fontan通道进行开窗,低蛋白血症和肠道蛋白丢失立即得到改善并消失。