Bours A F, Decat M, Gersdorff M
UCL, Cliniques Universitaires St Luc, Service ORL, Bruxelles, Belgique.
Rev Laryngol Otol Rhinol (Bord). 1997;118(4):271-2.
The syndrome in which velar myoclonus is associated with objective tinnitus is rare, and in the adult corresponds most commonly with a lesion in the dentato-rubro-olivary tract. In the child, no lesion can usually be found. The disorders of function resulting from this syndrome are very disabling. Many forms of treatment have been proposed, and the results have been found to be disappointing. The authors report the case of a child in which muscle relaxants were used to very good effect, and emphasize the fact that the natural history of the condition in childhood is one of spontaneous remission, so that aggressive treatment is not appropriate.
腭肌阵挛与客观性耳鸣相关的综合征很罕见，在成人中最常见于齿状红核橄榄束病变。在儿童中，通常找不到病变。该综合征导致的功能障碍极具致残性。人们提出了多种治疗方法，但结果令人失望。作者报告了一例使用肌肉松弛剂取得良好效果的儿童病例，并强调儿童期该病的自然病程是自发缓解，因此积极治疗并不合适。
