Asahina M, Kuwabara S, Nakajima M, Yamada T
Department of Neurology, School of Medicine, Chiba University, Japan.
Clin Neurol Neurosurg. 1998 Mar;100(1):53-5. doi: 10.1016/s0303-8467(97)00121-2.
A 47-year-old man showed progressive, symmetrical weakness in the limbs for 6 months. There was muscle atrophy, fasciculations, and acute denervation without motor conduction abnormalities below the elbows or knees, and motor neuron disease had once been suspected. However, compound muscle action potentials (CMAPs) after proximal stimulation showed an amplitude reduction between axilla and Erb's point for the median and ulnar nerves on both sides. His weakness as well as the amplitude reduction improved after administration of prednisolone. Demyelinative conduction abnormalities can be limited to the proximal segments for at least several months in a conduction equivalent to chronic inflammatory demyelinating polyneuropathy (CIDP).
一名47岁男性出现四肢进行性对称性无力6个月。存在肌肉萎缩、肌束震颤及急性去神经改变，肘或膝以下无运动传导异常，曾怀疑患有运动神经元病。然而，双侧正中神经和尺神经近端刺激后的复合肌肉动作电位（CMAPs）显示腋窝与Erb点之间波幅降低。给予泼尼松龙后，其无力症状及波幅降低情况有所改善。脱髓鞘性传导异常在相当于慢性炎症性脱髓鞘性多发性神经病（CIDP）的传导中，可局限于近端节段至少数月。
