Newson T, Cerio R, Leigh I, Jaywardhene D
Department of Paediatrics, Royal Children's Hospital, Flemington Road, Parkville, Victoria, 3052 Australia.
Pediatr Surg Int. 1998 Jul;13(5-6):447-8. doi: 10.1007/s003830050366.
Infantile myofibromatosis (IM) is a distinct but rare clinicopathological entity occurring in neonates and infants. It probably represents a rare soft-tissue tumour made up of undifferentiated myofibroblasts. Its recognition is important since it can be mistaken for a malignancy when, in fact, it has a generally benign prognosis with spontaneous regression. We describe the first case of an infant with IM presenting with acute intussusception due to gastrointestinal as well as the typical skin involvement.
婴儿肌纤维瘤病(IM)是一种发生于新生儿和婴儿的独特但罕见的临床病理实体。它可能代表一种由未分化肌成纤维细胞组成的罕见软组织肿瘤。认识到这一点很重要,因为它在实际上预后通常良好且可自发消退的情况下,可能被误诊为恶性肿瘤。我们描述了首例因胃肠道受累以及典型皮肤受累而出现急性肠套叠的婴儿肌纤维瘤病病例。