Dòmini M, Aquino A, Lima M, Federici S, Andriani G, Sardella L, Lelli Chiesa P, Dòmini R
Divisione di Chirurgia Pediatrica, Università G. D'Annunzio, Pescara, Italia.
Eur J Pediatr Surg. 1998 Jun;8(3):178-81. doi: 10.1055/s-2008-1071149.
Ectopic location of the vas deferens is a rare congenital anomaly with multiple variations. The frequent association with ano-rectal abnormalities and hypospadias is well known. We report two cases of a newborn and a 3-year-old child with ectopic vas deferens coupled with a left multicystic kidney without any ureteral structure. Furthermore, the latter had a contralateral vesicoureteral reflux and anal agenesis with recto-bulbar fistula. Our attempt with this report is to explain the development of such anomalous deferential outlet into the multicystic kidney, according to the most qualified theory of the Wolffian duct embryology.
输精管异位是一种罕见的先天性异常，有多种变异形式。其常与肛门直肠畸形和尿道下裂相关联，这一点已为人熟知。我们报告两例病例，一例为新生儿，另一例为3岁儿童，均患有输精管异位并伴有左侧多囊肾，且无任何输尿管结构。此外，后者还伴有对侧膀胱输尿管反流以及肛门闭锁并直肠球部瘘。我们撰写本报告的目的是根据最具权威性的中肾管胚胎学理论，解释这种异常的输精管开口通向多囊肾的发育过程。
