[“四苯”和“无苯”特殊产品在苯丙酮尿症患儿饮食治疗中的对比研究]

[Comparative study of special products "Tetraphen" and "Phenyl-free" in diet therapy of children with phenylketonuria].

作者信息

Bushueva T V, Vrzhesinskaia O A, Kodentsova V M, Rybakova E P, Denisova S N, Beketova N A, Taranova A G, Pereverzeva O G, Kharitonchik L A, Kopylova N V

出版信息

Vopr Pitan. 1998(2):14-8.

PMID:9680665

Abstract

Basing on the comparative clinical and biochemical evaluation of the usage of the specialized product "Tetraphen" (Russia) and early utilized product "Phenyl-Free" (USA) it has been shown that "Tetraphen" does not yield to "Phenyl-Free", while some of its parameters (energy value, carbohydrate content) even in the higher degree correspond to the physiologic requirements of this aged children suffering from phenylketonuria. Intake of this product in smaller doses completely covers their requirements for the basic food ingredients. High frequency of carotenoids insufficiency in children received both "Tetraphen" and "Phenyl-Free" demonstrate necessity of the diet correction by means of beta-carotene additional supplementation.

摘要

基于对俄罗斯专用产品“Tetraphen”和美国早期使用的产品“Phenyl-Free”的临床和生化比较评估，结果表明“Tetraphen”并不逊色于“Phenyl-Free”，而且其一些参数（能量值、碳水化合物含量）甚至在更高程度上符合患有苯丙酮尿症的大龄儿童的生理需求。以较小剂量摄入该产品完全满足了他们对基本食物成分的需求。接受“Tetraphen”和“Phenyl-Free”的儿童中类胡萝卜素缺乏的高频率表明，通过额外补充β-胡萝卜素进行饮食调整的必要性。