Choong C S, Liew K L, Tsai M J, Lin S M, Hsieh S P, Hsieh K S
Department of Pediatrics, Jen-Ai General Hospital, Pingtung, Taiwan, ROC.
Zhonghua Yi Xue Za Zhi (Taipei). 1998 Jun;61(6):362-6.
Intracardiac tumors are rare in neonates. Most of these lesions are rhabdomyomas and they occur almost exclusively during infancy. Rhabdomyomas are commonly associated with tuberous sclerosis and often involve the brain, kidneys and pancreas; they are frequently multiple and originate most commonly from the ventricular septum. Surgical intervention is indicated for rhabdomyoma with either mechanical cardiac obstruction or dysrhythmias resulting in symptoms or sudden death. A newborn with diffuse rhabdomyomatosis over the right atrium, right ventricle and left ventricle of the heart complicated with congestive heart failure and intractable supraventricular tachycardia is reported herein. No tuberous sclerosis or other organ involvement was noted. The tumor was resected.
心脏内肿瘤在新生儿中很罕见。这些病变大多是横纹肌瘤，几乎只发生在婴儿期。横纹肌瘤通常与结节性硬化症相关，常累及脑、肾和胰腺；它们通常是多发的，最常见于室间隔。对于伴有机械性心脏梗阻或导致症状或猝死的心律失常的横纹肌瘤，需要进行手术干预。本文报道了一名新生儿，其右心房、右心室和左心室出现弥漫性横纹肌瘤病，并发充血性心力衰竭和顽固性室上性心动过速。未发现结节性硬化症或其他器官受累。肿瘤已被切除。
