[Cholesteatoma of the middle ear in children. Clinical, developing and therapeutic study in a series of 215 consecutive cases].

A retrospective study of 215 cases of cholesteatoma in 199 children operated on from 1985 to 1996 was conducted. Mean age of the children was 9.6 years. Bilateral cholesteatoma was present in 32 cases (8%). The cause was congenital in 32 cases (16%), iatrogenic in 24 cases (11%) and secondary or acquired in 63%. The surgical procedure was a closed technique in 88%, an open technique with or without ossiculoplasty in 10%, and exclusion of the ear using the Rambo technique in exceptional cases (1%). The facial nerve was exposed in 17%. A labyrinth fistula was discovered in 4%, and an intracranial suppuration in only 0.5%. A secondary open procedure was required in 5 cases (2.5%) and secondary exclusion 3 times (1.5%). The ossicular chain was interrupted in 24.2% of the cases and ossicular rehabilitation was performed in 68% of the cases (39% type II, 29% type III), including 49% during the first procedure. At least 2 operations were needed in 62% of the children and 21% had 3 operations. Residual cholesteatomas were observed in 21.5% of all children in the series, 33% in those with a second operation. Recurrence rate was 10%. Mean hearing loss was 28 dB for a mean gain of 4 dB. Post-operative hearing capacity was socially useful in 64% of the cases, including 12% who had normal hearing. Labyrinthization was observed in 15 cases, including 4 cases with total hearing loss. These result are in general agreement with data in the literature. Our strategy is based on a closed procedure for cholesteatomy and systematic re-evaluation at 1 year. The open technique is useful for very extensive lesion on a narrow mastoid, either as second intention procedure or more rarely as a first intention procedure. Management in children differs from that in adults since in adults the destruction has usually progressed further in a mastoid which accepts an open procedure more readily.