Ikeda H, Kato M, Matsunaga A, Shimizu Y, Katsuura M, Hayasaka K
Department of Paediatrics, Yamagata University School of Medicine, Japan.
Eur J Pediatr. 1998 Jul;157(7):553-4. doi: 10.1007/s004310050876.
A 3-year-old boy with multiple sulphatase deficiency, complicated by a haemophagocytic syndrome, recovered with conventional treatment. Haemophagocytic syndrome can be a complication of many disorders including metabolic diseases, frequently triggered by intracellular viral and bacterial infections or even by drug administration.
一名患有多种硫酸酯酶缺乏症并伴有噬血细胞综合征的3岁男孩,经传统治疗后康复。噬血细胞综合征可能是包括代谢疾病在内的多种疾病的并发症,常由细胞内病毒和细菌感染甚至药物给药引发。