[原始肾神经外胚层肿瘤（PNET）。附病例报告]

[Primitive renal neuroectodermal tumor (PNET). Apropos of a case].

作者信息

Vigouroux V, Jeanne C, Comoz F, Auriault M L, Bottet P, Bensadoun H

机构信息

Service d'Urologie, Centre Hospitalo-Universitaire Côte de Nacre, Caen, France.

出版信息

Prog Urol. 1998 Jun;8(3):392-7.

PMID:9689673

Abstract

Renal primary neuroectodermal tumours (PNET) are exceptional and belong to the vast group of peripheral malignant primary neuroectodermal tumours (MPNT), the best known forms of which are Ewing's sarcoma of bone and Askin's thoracopulmonary tumour. In the light of a case, the authors discuss the clinical features, course, treatment and pathological characteristics, particularly the value of immunohistochemistry and cytogenetics, which demonstrate a specific chromosomal abnormality, the t (11;22) (q24;q12) translocation.

摘要

肾原发性神经外胚层肿瘤（PNET）较为罕见，属于外周恶性原发性神经外胚层肿瘤（MPNT）这一庞大类别，其中最知名的类型是骨尤文肉瘤和阿金胸肺肿瘤。结合一个病例，作者讨论了其临床特征、病程、治疗及病理特征，特别是免疫组织化学和细胞遗传学的价值，后者显示出一种特定的染色体异常，即t（11；22）（q24；q12）易位。