Majeed H A, Halabi I, al-Taleb O
Department of Pediatrics, Faculty of Medicine, University of Jordon, Amman.
Ann Trop Paediatr. 1998 Mar;18(1):13-5. doi: 10.1080/02724936.1998.11747919.
Recurrent hyperbilirubinaemia was described as a feature of familial Mediterranean fever in the 1950s and early 1960s. However, over the last 33 years only one case has been published. We present a 12-year-old Arab boy who developed recurrent hyperbilirubinaemia in the course of familial Mediterranean fever. His response to colchicine was excellent. Review of the literature reveals that hyperbilirubinaemia of familial Mediterranean fever has a distinct clinical picture characterized by concurrent peritonitis, minimal jaundice and short duration. Factors contributing to the paucity of reports in recent literature are discussed.
复发性高胆红素血症在20世纪50年代和60年代初被描述为家族性地中海热的一个特征。然而,在过去33年里仅发表过1例。我们报告1例12岁阿拉伯男孩,其在家族性地中海热病程中出现复发性高胆红素血症。他对秋水仙碱反应良好。文献回顾显示,家族性地中海热的高胆红素血症具有独特的临床表现,其特征为并发腹膜炎、黄疸轻微且持续时间短。本文讨论了导致近期文献中报道稀少的因素。