A case of epidermoid cyst arising from the rostral neuropore: case report.

OBJECTIVE AND IMPORTANCE

Supratentorial epidermoid cysts located on the midline are very rare. We describe the first case of such a cyst arising from the rostral neuropore.

CLINICAL PRESENTATION AND INTERVENTION

We report a patient suffering from seizures and progressive frontal syndrome and presenting with a huge cyst developed in the midline at the rostralmost part of the corpus callosum. The patient was operated on, and the cyst was found to be epidermoid.

CONCLUSION

Only six cases of supracallosal epidermoid cysts have been reported. In our case, the involved region was located at the exact limit between lamina terminalis and corpus callosum. This region corresponds to the place of the closing rostral neuropore during embryogenesis. We thus propose that the cyst arises from the rostral neuropore and that its eventual deep location is explained by the complex morphogenetic movements affecting the dorsal region of the telencephalic vesicle.