Heymans O, Gebhart M, Alexiou J, Sokolow Y
Department of Orthopedics, J. Bordet Institute, Bruxelles.
Acta Clin Belg. 1998 Jun;53(3):189-92.
Camurati-Engelmann disease is an uncommon condition, radiologically characterized by symmetric diaphyseal sclerosis involving the tubular bones. Clinical features include limb pain, muscle weakness, waddling gait and sometimes deafness. The evaluation is made by conjunction of radiographic and scintigraphic data. Corticosteroids and analgesics improve the quality of life, decrease the pain but do not alter the course of the disease. The evolution is unpredictable. The history of a 23 year old male with such a disorder is presented hereafter. His clinical course shows a very good response to the administration of corticosteroids, whereas no improvement is observed as far as the radiographic and isotopic features are concerned.
卡姆拉蒂-恩格尔曼病是一种罕见疾病，其放射学特征为累及管状骨的对称性骨干硬化。临床特征包括肢体疼痛、肌肉无力、蹒跚步态，有时还会耳聋。通过结合放射学和闪烁扫描数据进行评估。皮质类固醇和镇痛药可改善生活质量、减轻疼痛，但不会改变疾病进程。病情发展不可预测。以下介绍一名患有这种疾病的23岁男性的病史。他的临床病程显示对皮质类固醇治疗反应良好，但就放射学和同位素特征而言未观察到改善。
