Freedom R M, Hashmi A
Department of Paediatrics, The Hospital for Sick Children and University of Toronto Faculty of Medicine, Ontario, Canada.
Ann Thorac Surg. 1998 Aug;66(2):681-2. doi: 10.1016/s0003-4975(98)00617-1.
There is now a considerable literature that babies with right atrial isomerism have a poor outcome. The reasons for this are complex and multifactorial, but may be related at least in part to intrinsically small and abnormal pulmonary veins. We reviewed a series of consecutive patients seen at a single institution and found that babies with right atrial isomerism, severe pulmonary outflow tract obstruction or atresia, and total anomalous obstructed pulmonary veins had a grim outlook, especially those requiring operation in the neonatal period. Others have reported a similarly concerning outcome.
目前有大量文献表明，患有右心房异构的婴儿预后不良。其原因复杂且多因素，但可能至少部分与肺静脉本身细小和异常有关。我们回顾了在单一机构连续就诊的一系列患者，发现患有右心房异构、严重的肺流出道梗阻或闭锁以及完全性肺静脉异位引流且梗阻的婴儿预后严峻，尤其是那些在新生儿期需要手术的婴儿。其他人也报告了类似令人担忧的结果。
