Michel J L, Secchi T, Balme B, Barrut D, Thomas L, Moulin G
Service de Dermatologie, Hôpital de l'Antiquaille, Lyon.
Ann Dermatol Venereol. 1997;124(9):623-5.
Eccrine angiomatous hamartoma is an uncommon skin disease with vascular and sudoral components: less than thirty cases have been reported in the literature.
A 3.5 month-old female infant developed a painful angiomatous plaque on the abdomen which was first seen 15 days after birth. Histology showed numerous vessels and eccrine sudoral glands in the dermis. Exeresis could not be complete and was followed for 15 years. There has been a slight hyperpigmentation with localized hyperhidrosis over the plaque. This hypersudation confirms the diagnosis which could not be confirmed on the initial biopsies.
This case of congenital eccrine angiomatous hamartoma could only be diagnosed late in the clinical course. This is the first case report on the abdomen, 80 p. 100 of the previous reports were on the limbs. After a 15 year follow-up, there was no progression of the hamartoma and pain regressed gradually. Without secondary development of localized hyperhidrosis, the diagnosis could not have been made. Careful comparison of pathology findings and clinical expression are essential for the diagnosis of eccrine angiomatous hamartoma.
小汗腺血管瘤性错构瘤是一种罕见的皮肤疾病，具有血管和汗腺成分：文献报道不足30例。
一名3.5个月大的女婴腹部出现一个疼痛性血管瘤性斑块，出生后15天首次发现。组织学检查显示真皮内有大量血管和小汗腺。手术切除无法彻底清除，随后进行了15年的随访。斑块处有轻微色素沉着和局限性多汗。这种多汗症证实了最初活检未能确诊的诊断。
这例先天性小汗腺血管瘤性错构瘤在临床过程中诊断较晚。这是第一例关于腹部的病例报告，之前报告的80%病例发生在四肢。经过15年的随访，错构瘤无进展，疼痛逐渐消退。若无局限性多汗症的继发表现，则无法做出诊断。仔细比较病理结果和临床表现对于小汗腺血管瘤性错构瘤的诊断至关重要。
