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韦格纳肉芽肿病的脉络膜受累:一例报告

Choroidal involvement in Wegener's granulomatosis: a case report.

作者信息

Lee A F, Wu J S, Huang D F, Chung Y M, Yang Y K

机构信息

Department of Ophthalmology, Veterans General Hospital-Taipei, Taiwan, ROC.

出版信息

Zhonghua Yi Xue Za Zhi (Taipei). 1998 Aug;61(8):496-9.

PMID:9745168
Abstract

Wegener's granulomatosis is a necrotizing, granulomatous vasculitis. It usually causes sinusitis, pneumonitis and glomerulonephritis. The common ocular manifestations include conjunctivitis, scleritis, peripheral keratitis and orbital inflammation. We report the case of a 50-year-old woman with Wegener's granulomatosis and very severe ocular complications who underwent bilateral enucleation. The pathologic findings of the eyeballs revealed granulomatous necrotizing scleritis, perivasculitis and granulomatous choroiditis. The last, as far as we know, has not yet been reported.

摘要

韦格纳肉芽肿是一种坏死性肉芽肿性血管炎。它通常会引发鼻窦炎、肺炎和肾小球肾炎。常见的眼部表现包括结膜炎、巩膜炎、周边角膜炎和眼眶炎症。我们报告了一例50岁患有韦格纳肉芽肿且伴有非常严重眼部并发症的女性患者,该患者接受了双侧眼球摘除术。眼球的病理检查结果显示为肉芽肿性坏死性巩膜炎、血管周围炎和肉芽肿性脉络膜炎。据我们所知,后者此前尚未见报道。

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