Platokouki H, Aronis S, Mitsika A, Keramidas D, Harokopos E
Hemostasis Unit, Athens University, Aghia Sophia Children's Hospital, Greece.
Acta Paediatr Jpn. 1998 Aug;40(4):381-4. doi: 10.1111/j.1442-200x.1998.tb01954.x.
The case of a 7-year-old girl with a 2 year history of easy bruising associated with thrombocytopenia is reported. On admission she presented with ecchymoses, abdominal distention and splenomegaly. Hemostasis investigation revealed a consumption coagulopathy. Several radiological studies failed to confirm the diagnosis of diffuse splenic and visceral hemangiomatosis, which was eventually established by an explorative laparotomy. Platelet count and the other coagulation abnormalities progressively returned to normal after splenectomy, although the remaining hemangiomas were extensive.
