Gatinel D, Larroche C, Fanjkuchen F, Chaine G, Guillevin L
Service d'Ophtalmologie, Hôpital Avicenne, Bobigny, France.
J Fr Ophtalmol. 1998 Feb;21(2):133-41.
POEMS syndrome is a multisystem disorder associated with plasma cell dyscrasia. Papilloedema is a feature of this syndrome with an incidence ranging from 33% to 84% in published reports. Its pathogenesis remains unclear. We present an observation that clearly demonstrates the difficulties to diagnose this affection. POEMS syndrome can be accepted as one of the various etiologies of papilloedema. Considering this observation and the recent publications, different pathological hypothesis are reviewed.
POEMS综合征是一种与浆细胞异常增生相关的多系统疾病。视乳头水肿是该综合征的一个特征,在已发表的报告中,其发生率在33%至84%之间。其发病机制尚不清楚。我们展示了一项观察结果,该结果清楚地表明了诊断这种疾病的困难。POEMS综合征可被视为视乳头水肿的多种病因之一。考虑到这一观察结果和近期的出版物,我们对不同的病理假说进行了综述。