Khalil M R
Organkirurgisk afdeling, Sygehus Fyn, Middelfart.
Ugeskr Laeger. 1998 Sep 14;160(38):5517-8.
Neurofibromatosis is a relatively common genetic disorder of the peripheral and central nervous systems. Benign or malignant tumours may occur in different organs. Visceral tumours arising in the neural plexus of the intestinal wall may cause ulceration, bleeding, obstruction, perforation and palpable abdominal masses. In this paper a case of chronic anaemia due to a chronically bleeding intestinal neurofibroma is presented in a woman who had undergone intestinal resection. Histopathological analysis showed a neurofibroma with malignant transformation and a liver metastasis.
神经纤维瘤病是一种相对常见的周围和中枢神经系统遗传性疾病。良性或恶性肿瘤可能发生于不同器官。起源于肠壁神经丛的内脏肿瘤可导致溃疡、出血、梗阻、穿孔及可触及的腹部肿块。本文报道一例经肠切除术后的女性患者,其因肠道神经纤维瘤慢性出血导致慢性贫血。组织病理学分析显示神经纤维瘤发生恶变并伴有肝转移。