华氏巨球蛋白血症伴肺淀粉样变性
Waldenström's macroglobulinemia with pulmonary amyloidosis.
作者信息
Zatloukal P, Bezdícek P, Schimonová M, Havlícek F, Tesarová P, Slováková A
机构信息
Department of Pneumology and Thoracic Surgery, Third Faculty of Medicine, First Department of Tuberculosis and Respiratory Diseases, Pathology and Hematology, First Faculty of Medicine, Charles University, Prague, Czech Republic.
出版信息
Respiration. 1998;65(5):414-6. doi: 10.1159/000029306.
We present a case of AL-type amyloidosis involving pulmonary parenchyma and hilar and mediastinal lymph nodes in a patient with Waldenström's macroglobulinemia. Direct infiltration of pulmonary parenchyma by lymphocytes and plasma cells is an important factor in the etiology and pathogenesis of pulmonary manifestations of the disease. Despite detailed examination, we did not find amyloid depositions in any extrapulmonary site.
我们报告一例患有华氏巨球蛋白血症的患者，其AL型淀粉样变性累及肺实质、肺门和纵隔淋巴结。淋巴细胞和浆细胞直接浸润肺实质是该疾病肺部表现的病因和发病机制中的一个重要因素。尽管进行了详细检查，但我们未在任何肺外部位发现淀粉样蛋白沉积。
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