Imai M, Yamaguchi M, Ohashi H, Oshima Y, Kawaraya N, Ogawa K
Department of Cardio-Thoracic Surgery, Kobe Children's Hospital, Japan.
Jpn J Thorac Cardiovasc Surg. 1998 Aug;46(8):793-7. doi: 10.1007/BF03217824.
We report a rare case of corrected transposition of great arteries and mitral atresia associated with double aoric arch. The patient showed polypnea and cyanosis soon after birth. She underwent balloon atrioseptostomy at the age of 18 days and pulmonary artery banding (PAB) at 24 days. But she showed severe persistent stridor after PAB. Esophagography and left counter-current aortography revealed double aortic arch. At the age of 49 days, division of the left lesser arch and ligation of patent ductus arteriosus were performed through left lateral thoracotomy. Stridor disappeared completely following operation. She underwent total cavopulmonary connection using a 18 mm Gore-Tex graft as intraatrial conduit concomitant with pacemaker implantation at the age of 8 years. Postoperative course was uneventful. To our knowledge, this is the first successful case report of surgical correction of corrected transposition of great arteries and mitral atresia associated with double aoric arch.
我们报告一例罕见的矫正型大动脉转位合并二尖瓣闭锁并伴有双主动脉弓的病例。该患者出生后不久即出现气促和发绀。她在18日龄时接受了球囊房间隔造口术，并在24日龄时接受了肺动脉环扎术（PAB）。但在PAB术后她出现了严重的持续性喘鸣。食管造影和左心逆行主动脉造影显示为双主动脉弓。在49日龄时，通过左外侧开胸术进行了左小弓离断和动脉导管未闭结扎术。术后喘鸣完全消失。她在8岁时使用18mm Gore-Tex移植物作为心房内管道进行了全腔肺连接，并同时植入了起搏器。术后过程顺利。据我们所知，这是首例成功手术矫正矫正型大动脉转位合并二尖瓣闭锁并伴有双主动脉弓的病例报告。
