Berio A, Piazzi A
Chair of Pediatrics, University of Genoa, Institute G. Gaslini, Italy.
Panminerva Med. 1998 Sep;40(3):244-6.
In a case of typical cystinuria type I with left kidney hypoplasia and bilateral calculosis, calculi were dissolved by means of alpha-mercapto-propionyl-glycine and prophylaxis of the calculosis was performed by the same drug continuously administered in two divided doses (10-4 mg.kg-1.day-1) for 9 years, without urolithiasis. Then, the alpha-mercaptopropionyl-glycine every other day in one dose, 4 mg.kg-1.day-1, for two years was administered without calculosis. The arbitrary discontinuation of the drug by the patient was followed after 6 months from a right ureteral calculosis with transitory renal insufficiency. In our case the administration of a low dose of alpha-mercapto-propionyl-glycine every other day was useful in cystine calculosis prophylaxis.
在一例典型的I型胱氨酸尿症合并左肾发育不全及双侧结石病患者中,通过α-巯基丙酰甘氨酸溶解结石,并使用同一药物以分两次给药(10 - 4毫克·千克⁻¹·天⁻¹)的方式持续进行结石病预防,长达9年,期间未出现尿路结石。之后,每隔一天服用一次α-巯基丙酰甘氨酸,剂量为4毫克·千克⁻¹·天⁻¹,持续两年,未出现结石。患者自行停药6个月后出现右侧输尿管结石并伴有短暂性肾功能不全。在我们的病例中,每隔一天给予低剂量的α-巯基丙酰甘氨酸对预防胱氨酸结石病是有效的。