Chan S K, Ng S K, Cho A M, Oh T E
Department of Anaesthesia and Intensive Care, Chinese University of Hong Kong, Prince of Wales Hospital.
Anaesth Intensive Care. 1998 Oct;26(5):586-9. doi: 10.1177/0310057X9802600520.
Maffucci's syndrome is a rare, congenital disease due to neuro-ectodermal dysplasia and is characterized by enchondromatosis and multiple soft tissue haemangiomata. A case of Maffucci's syndrome with haemangiomata along the upper airways requiring laser surgery is described. The literature on Maffucci's syndrome is reviewed.
马富西综合征是一种罕见的先天性疾病,由神经外胚层发育异常引起,其特征为内生软骨瘤病和多发性软组织血管瘤。本文描述了一例伴有上呼吸道血管瘤且需要激光手术治疗的马富西综合征病例,并对马富西综合征的相关文献进行了综述。