Gumprecht H, Lumenta C B
Neurochirurgische Abteilung, Akademisches Lehrkrankenhaus München-Bogenhausen, Technische Universität München.
Zentralbl Neurochir. 1998;59(3):181-4.
A 25 years old female person suffered from v. Hippel-Lindau disease with three manifestations within the central nervous system (cerebellum, nerve root C1 and Medulla oblongata). Pancreatic cysts, a cyst and a tumour of the kidney were diagnosed as well. In a first operation, the large cerebella's tumour and the small haemangioblastoma of the nerve root C1 were removed via a suboccipital craniectomy. A few weeks later, after the patient had made a good recovery, the tumour at the craniocervical junction was removed through a far lateral approach. The postoperative course was without complications. The MRI control seven months after surgery was free of tumour and the young person was in a good clinical condition, without neurological deficit.
一名25岁女性患有希佩尔-林道病,中枢神经系统出现三种表现(小脑、C1神经根和延髓)。同时还诊断出胰腺囊肿、肾囊肿和肾肿瘤。在首次手术中,通过枕下颅骨切除术切除了小脑的大肿瘤和C1神经根的小血管母细胞瘤。几周后,患者恢复良好,通过远外侧入路切除了颅颈交界处的肿瘤。术后过程无并发症。术后七个月的MRI检查未发现肿瘤,该年轻人临床状况良好,无神经功能缺损。