Lee J, Song S Y, Park C S, Kim B
Department of Diagnostic Pathology, Sungkyunkwan University, College of Medicine, Samsung Medical Center, Seoul, Korea.
Pathol Int. 1998 Nov;48(11):902-6. doi: 10.1111/j.1440-1827.1998.tb03859.x.
Müllerian cyst of the mesentery and retroperitoneum is an extremely rare disease entity. Only two photomicrograph reports have been published. A 47-year-old Korean woman presented with abdominal distention. A mesenteric cystic mass, measuring 25 x 23 x 18 cm, was found between the liver and right adnexa without any connection with adjacent organs. The cyst was multilocular with gray-white, rubbery walls of relatively uniform 0.2 cm thickness. Microscopically, the lining cells were ciliated and cuboidal to low columnar with an incomplete lining of smooth muscle bundles, adipose tissues, lymphovascular spaces, and lymphocytic aggregates. Ultrastructurally, the lining cells had intercellular junctions, and cilia or microvilli on their luminal surface. The lining cells were immunoreactive for cytokeratin, epithelial membrane antigen and vimentin. To the best of our knowledge, this is the first demonstration of ultrastructural and immunohistochemical findings of Müllerian cyst of the mesentery and retroperitoneum in the English literature.
肠系膜及腹膜后苗勒氏管囊肿是一种极为罕见的疾病实体。仅发表过两篇显微照片报告。一名47岁的韩国女性因腹胀就诊。在肝脏与右附件之间发现一个大小为25×23×18 cm的肠系膜囊性肿物，与相邻器官无任何连接。囊肿为多房性，灰白色，囊壁呈橡胶样，相对均匀，厚度为0.2 cm。显微镜下，内衬细胞为纤毛状，呈立方形至低柱状，平滑肌束、脂肪组织、淋巴管腔隙和淋巴细胞聚集呈不完全内衬。超微结构显示，内衬细胞有细胞间连接，其腔面有纤毛或微绒毛。内衬细胞对细胞角蛋白、上皮膜抗原和波形蛋白呈免疫反应阳性。据我们所知，这是英文文献中首次展示肠系膜及腹膜后苗勒氏管囊肿的超微结构和免疫组化结果。
