Kumar P R, Rakshak A D, Rajagopal P, Padmanabhan T N, Rao D S, Jaishanker S
Department of Cardiac Radiology, Nizam's Institute of Medical Sciences, Hyderabad.
Indian Heart J. 1998 Jul-Aug;50(4):446-50.
Tetralogy of Fallot with restrictive ventricular septal defect and suprasystemic right ventricular pressure is an uncommon anomaly with high mortality rate. Very few such cases have been reported pre-operatively. This report describes echocardiographic features of five patients with restrictive ventricular septal defect due to flap valve in tetralogy of Fallot. In all the five cases, accessory or excessive tricuspid valve tissue obstructed the defect. Recognition of restrictive ventricular septal defect in tetralogy of Fallot is important because it appears to have poor prognosis.
伴有限制性室间隔缺损和右心室压力高于体循环压力的法洛四联症是一种死亡率高的罕见畸形。术前报道的此类病例极少。本报告描述了5例法洛四联症中因瓣叶导致限制性室间隔缺损患者的超声心动图特征。在所有5例病例中，三尖瓣附属组织或多余组织阻塞了缺损处。认识到法洛四联症中的限制性室间隔缺损很重要，因为其预后似乎较差。
