Duodenal duplication cyst communicating with an accessory pancreatic duct of Santorini.

A 16 year-old girl with recurrent attacks of acute pancreatitis and upper gastrointestinal bleeding was found to have an aberrant pancreatic duct communicating with a duodenal duplication cyst and a pancreatic pseudocyst on endoscopic retrograde pancreatography (ERP). A partial gastrectomy combined with resection of the aberrant pancreas was performed. The patient is doing well without any problems 17 years after surgery. ERP was of great value in diagnosing this rare disease. Gastroduodenal duplication cysts communicating with the pancreatic duct are rare; only 21 cases, including our own, have been reported in the English-language literature since 1958.