Fuse T, Yamada K, Kamiya K, Inagaki H
Department of Neurosurgery, Nagoya City University Medical School, Nagoya, Japan.
Surg Neurol. 1998 Nov;50(5):431-6. doi: 10.1016/s0090-3019(97)00280-2.
Neurenteric cysts are rare endothelium-lined structures. Two patients with symptomatic neurenteric cysts at the craniovertebral junction are presented.
Intermittent progression of neurologic symptoms delayed diagnosis for both patients. In one case, marked enlargement of the cyst was detected on serial imaging studies, and pathological examination of the excised lesion indicated rupture of the cyst. These cysts were totally resected by transoral or suboccipital approaches, as they were not firmly adherent to surrounding neural structures. The diagnosis of neurenteric cyst was confirmed by immunohistochemical analysis of the cyst wall.
In view of the clinical course of these patients, we recommend early surgical resection of neurenteric cysts located at the craniovertebral junction.
神经肠囊肿是罕见的内衬内皮的结构。本文介绍了两名在颅颈交界处患有症状性神经肠囊肿的患者。
两名患者的神经症状间歇性进展导致诊断延迟。在一个病例中，连续影像学检查发现囊肿明显增大，切除病变的病理检查显示囊肿破裂。由于这些囊肿未与周围神经结构紧密粘连，因此通过经口或枕下入路将其完全切除。通过对囊肿壁的免疫组织化学分析证实了神经肠囊肿的诊断。
鉴于这些患者的临床病程，我们建议对位于颅颈交界处的神经肠囊肿尽早进行手术切除。
