Azcuna J I, Cabrera A, Chouza M, Bilbao F, Pastor E, Oñate Landa A
An Esp Pediatr. 1976 Jul-Aug;9(4):364-72.
In this article we try to show the value of radiography and angiocardiography in primary endocardial fibroelastosis. The 20 CASEs studied in this report, were angiocardiographically and/or necropsically proved. In spite of different opinions, we think that it is possible to reach an approximate diagnosis of this condition if we use the clinical and angiohemodinamic examinations. On the other hand, it is necessary to point out that pathology is characteristic. The most important radiological signs were cardiomegaly, together with venocapilar congestion, both of variable magnitude, and dependent on the degree of cardiac insufficiency. By means of angiocardiography we could appreciate a great dilatation and hypertrophy of the left ventricle and a reduction of the mobility and distensibility of this cavity along the cardiac cycle.
在本文中，我们试图展示放射学和心血管造影在原发性心内膜弹力纤维增生症中的价值。本报告中研究的20例病例均经心血管造影和/或尸检证实。尽管存在不同观点，但我们认为，如果采用临床和血管血液动力学检查，有可能对这种疾病做出大致诊断。另一方面，必须指出病理学具有特征性。最重要的放射学征象是心脏扩大，伴有不同程度的肺静脉毛细血管充血，且取决于心脏功能不全的程度。通过心血管造影，我们可以观察到左心室明显扩张和肥厚，以及该腔室在心动周期中活动度和可扩张性降低。
