Carbone R, Dessanti P, Sblendorio L
Dept of Bronchology, Regional Hospital, Aosta, Italy.
Monaldi Arch Chest Dis. 1998 Oct;53(5):530-2.
We report a very, rare case of idiopathic pulmonary haemosiderosis (IPH) occurring in a 68 yr old patient. Following alveolar haemorrhage onset, the diagnosis was obtained by a process of elimination, after clinical, endoscopic, cytohistological and laboratory investigations. The immunoglobulin G directed against myeloperoxidase antigen (C-ANCA), which was detected, can be regarded as indicative of an occult vasculitis to be followed up. Current therapy and perspectives for idiopathic pulmonary haemosiderosis patients are discussed herein.
我们报告了一例非常罕见的特发性肺含铁血黄素沉着症（IPH），发生在一名68岁的患者身上。在肺泡出血发作后，经过临床、内镜、细胞组织学和实验室检查，通过排除法做出了诊断。检测到的针对髓过氧化物酶抗原的免疫球蛋白G（C-ANCA）可被视为隐匿性血管炎的指标，需进行随访。本文讨论了特发性肺含铁血黄素沉着症患者的当前治疗方法和前景。
