骨髓增生异常综合征中的嗜酸性脓疱性毛囊炎（小藤病）

Eosinophilic pustular folliculitis (Ofuji's disease) in myelodysplastic syndrome.

作者信息

Jang K A, Chung S T, Choi J H, Sung K J, Moon K C, Koh J K

机构信息

Department of Dermatology, Asan Medical Center, College of Medicine, University of Ulsan, Seoul, Korea.

出版信息

J Dermatol. 1998 Nov;25(11):742-6. doi: 10.1111/j.1346-8138.1998.tb02494.x.

DOI:10.1111/j.1346-8138.1998.tb02494.x

PMID:9863288

Abstract

We describe a case of eosinophilic pustular folliculitis (EPF, Ofuji's disease) in a 12-year-old male who suffered from myelodysplastic syndrome. Bone marrow study revealed an increase in the eosinophil cell line without peripheral blood eosinophilia in our case. We suggest that the immunologic abberations ascribed to myelodysplastic syndrome and the increase in the eosinophil cell line in the bone marrow might play roles in the development of EPF in our case.

摘要

我们描述了一例患有骨髓增生异常综合征的12岁男性嗜酸性脓疱性毛囊炎（EPF，Ofuji病）病例。骨髓研究显示，在我们的病例中，嗜酸性粒细胞系增加，但外周血嗜酸性粒细胞未增多。我们认为，与骨髓增生异常综合征相关的免疫异常以及骨髓中嗜酸性粒细胞系的增加可能在我们这个病例的EPF发病过程中起到了作用。