Lacrimal gland choristoma of the iris.

Intraocular lacrimal gland tissue is an extremely rare choristoma. A newborn girl was seen with a fleshy, vascular tumor arising from the peripheral iris and the anterior chamber angle. The tumor was treated with topical steroids on suspicion of a juvenile xanthogranuloma; later, it grew slightly and a secondary glaucoma developed. Histopathological examination of the resected tumor showed lacrimal gland tissue in the iris. Twelve cases of intraocular lacrimal gland tissue have been reported in the literature.