Cursiefen C, Schlötzer-Schrehardt U, Holbach L M, Naumann G O
Department of Ophthalmology, University Eye Hospital, Friedrich-Alexander-University Erlangen-Nürnberg, Germany.
Arch Ophthalmol. 1999 Jan;117(1):113-6. doi: 10.1001/archopht.117.1.113.
Adenomas of the nonpigmented ciliary epithelium are rare tumors and are difficult to differentiate from amelanotic malignant melanomas of the ciliary body. We describe a 62-year-old woman with a nonpigmented, vascularized iris tumor with small satellites involving the anterior chamber angle. Clinically, an amelanotic, tapioca, malignant melanoma of the iris was suggested although the blood-aqueous barrier was intact. A block excision of 7.5 mm, a tectonic corneoscleral graft, and a simultaneous extracapsular cataract extraction with implantation of a posterior chamber lens were performed. Histopathologic and electron microscopic studies revealed an adenoma of the nonpigmented ciliary epithelium. Postoperative visual acuity was 20/40 OD after 6 weeks. An adenoma of the nonpigmented ciliary epithelium may mimic an amelanotic malignant melanoma of the iris and should be considered in its differential diagnosis.
无色素睫状体上皮腺瘤是一种罕见肿瘤，很难与睫状体无黑色素恶性黑色素瘤相鉴别。我们描述了一名62岁女性，患有一个无色素、血管化的虹膜肿瘤，伴有累及前房角的小结节。临床上，尽管血-房水屏障完整，但提示为虹膜无黑色素、木薯样恶性黑色素瘤。进行了7.5毫米的整块切除、结构性角巩膜移植，以及同期囊外白内障摘除联合后房型人工晶状体植入术。组织病理学和电子显微镜研究显示为无色素睫状体上皮腺瘤。6周后右眼视力为20/40。无色素睫状体上皮腺瘤可能酷似虹膜无黑色素恶性黑色素瘤，在鉴别诊断中应予以考虑。
