Sakai Y, Nasu T
Acta Pathol Jpn. 1976 Sep;26(5):637-47. doi: 10.1111/j.1440-1827.1976.tb00521.x.
This report presents the first autopsy case in Japan of idiopathic retroperitoneal fibrosis which had developed in a 71-year-old man. The clinical course was of extremely long duration of more than 10 years. Malignancy was suspected on biopsy, and at one stage chylous ascites developed. The cause of this retroperitoneal fibrosis could not be determined, but it is considered that the vicious circle of inflammatory processes such as cellulitis and lymphangitis in the retroperitoneum and lymphedema as well as lymphorrhage attributable to mechanical lymphatic obstruction brought about the retroperitoneal fibrosis.
本报告介绍了日本首例发生在一名71岁男性身上的特发性腹膜后纤维化尸检病例。临床病程持续时间极长，超过10年。活检时怀疑有恶性病变，且曾一度出现乳糜性腹水。该腹膜后纤维化的病因无法确定，但据认为，腹膜后蜂窝织炎和淋巴管炎等炎症过程、淋巴水肿以及机械性淋巴管阻塞所致的淋巴出血形成的恶性循环导致了腹膜后纤维化。
