Katz J S, Houroupian D, Ross M A
Department of Neurology, Department of Veterans Affairs, Stanford University School of Medicine, Palo Alto, California 94304, USA.
Muscle Nerve. 1999 Mar;22(3):404-7. doi: 10.1002/(sici)1097-4598(199903)22:3<404::aid-mus15>3.0.co;2-e.
We report two patients with multisystem neuronal involvement associated with sicca complex. One had a lower motor neuron syndrome combined with a flaccid bladder and rectum. The second patient had unilateral hearing loss, sensory neuronopathy, Adie's pupils, upper motor neuron signs, and autopsy-proven anterior horn cell degeneration. Our cases lead us to propose that the spectrum of neuronal involvement occurring with sicca syndrome may be wider than is currently appreciated.
