Hami B B, Le Gall F, Jouan H, Almange C, Loire R
Laboratoire d'Anatomie Pathologique B, CHR, Hôpital Pontchaillou, 2, Rennes, France.
Arch Anat Cytol Pathol. 1999;47(1):53-6.
Papillary fibroelastoma is a seldom reported tumour. It usually occurs in adults and develops on the aortic and mitral valves. It is not different of giant Lambl excrescences and differential diagnostic can be difficult with the myxoma. Its systematic surgical ablation is justified by the important risk of embolic complications. It has rarely been reported in children. We report a case peculiar by fortuitous diagnostic, tricuspid site, large size and occurrence in a 3-year old child.
乳头状纤维弹性瘤是一种报道较少的肿瘤。它通常发生于成年人,多见于主动脉瓣和二尖瓣。它与巨大的兰氏赘生物并无差异,与黏液瘤的鉴别诊断可能存在困难。因其存在发生栓塞并发症的重大风险,故进行系统性手术切除是合理的。儿童病例鲜有报道。我们报告一例具有偶然诊断、三尖瓣部位、瘤体较大以及发生于一名3岁儿童等特殊情况的病例。