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[我们在闭塞性细支气管炎机化性肺炎(BOOP)方面的经验:个人经历]

[Our experience in bronchiolitis obliterans organising pneumonia (BOOP): personal experience].

作者信息

Remiszewski P, Słodkowska J, Pawlicka L, Płodziszewska M, Załeska J, Dorosz P, Rowińska-Zakrzewska E

机构信息

III Kliniki Gruźlicy i Chorb Płuc.

出版信息

Pol Merkur Lekarski. 1998 Dec;5(30):372-6.

PMID:10101528
Abstract

BOOP is a disease with characteristic histology features which can occur as a secondary lung reaction to the various toxic agents or as a primary idiopathic disease. Idiopathic form of BOOP is a rare disease and may be found in 6-7 patients of 100,000 hospital admissions. We described 3 patients with idiopathic BOOP confirmed by the histologic lung examination. The time from the beginning of symptoms till the microscopical diagnosis ranged from 6 to 12 months. At the beginning of the disease the patients had symptoms compatible with the respiratory infection. In one of the patients the clinical course of the disease had a progressive character. In two patients spontaneous regression of radiological lung lesions was observed. This regression was however only temporary in one of them. In two cases treated by steroids regression of lung lesions was noticed.

摘要

闭塞性细支气管炎伴机化性肺炎(BOOP)是一种具有特征性组织学特征的疾病,它可作为肺部对各种毒性因子的继发性反应出现,也可作为原发性特发性疾病出现。特发性BOOP是一种罕见疾病,每10万例住院患者中可能有6至7例。我们描述了3例经肺组织学检查确诊的特发性BOOP患者。从症状出现到显微镜诊断的时间为6至12个月。疾病初期,患者有与呼吸道感染相符的症状。其中1例患者疾病的临床病程呈进行性。2例患者观察到肺部放射学病变自发消退。然而,其中1例的消退只是暂时的。2例接受类固醇治疗的患者肺部病变出现消退。

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Pol Merkur Lekarski. 1998 Dec;5(30):372-6.
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